Ukunyuka kweentso (uRussell Silver Syndrome) ngenye yezinto ezingabonakaliyo zokuzalwa kweengtso. Ubonakaliswe ngokungahambi ngokupheleleyo kwelungu okanye ukuphuhliswa kwayo. Le ntsholongwane inokubangela ukubonakala kwe-pyelonephritis, nephrolithiasis kunye nomfutho wegazi.
Iimpawu zokupheka kweengso
I-aplasia yeentso iyenzeka xa umsele weemethanephros ungakhuli ukuya kwi-metanephrogenic blastema. I-ureter ingaba yinto eqhelekileyo kwaye imfutshane. Kwiimeko ezinqabileyo, akakho ngokupheleleyo. Uphawu oluqhelekileyo lwe-aplasia yezintso zesinxele okanye sokunene linciphisa kwisixa somchamo okanye ukungabi khona kwayo. Kwakhona, ukungabikho kwenye inxalenye yeli qumrhu kuvumela i- colic coal -side (oku kuhlaselwa intlungu ebuhlungu ehambisana ne-anuria). Ayikho enye impawu kule ngozi.
Ukuxilongwa kwezintso zepilisi
Ukufumanisa i-aplasia yeentso zesinxele okanye sokunene, kubalulekile ukwenza uvavanyo lwe-ultrasound lwesigxina somzimba. Kwakhona, ubukho beziko elingaphantsi kokuphuhliswa okanye ukungabikho kwayo kungagqitywa ngokusebenzisa:
- i-tomography ecatshulwa;
- ingqungquthela yeengcingo;
- Utyando oluthile.
44.0-80.0 i-μmol / L yinto evamile yokudala i-creatinine kwigazi lomfazi, kodwa nge-aplasia yeentso le ngcaciso inganciphisa. Ngoko ke, ukuba kukho iimpawu zolu hlobo lentsholongwane, kufuneka ufune ukuhlolwa kwegazi.
Unyango lwepsosia
I-Aplasia yeentso ezilungileyo okanye ezisekho ngokuqhelekileyo ayifuni unyango lwonyango. Ukuze ulondoloze impilo yabantu kwiimeko eziqhelekileyo, kufuneka ulandele ukutya okwenzelwe ukunciphisa umthwalo kwizintso zesibini. Ukuba isiguli sigxininisekile, kufuneka ukuba athathe i-diuretics.
Ukungenelela ngoncedo kunye ne-aplasia kusetyenziswa kuphela xa:
- ukuphuhliswa komfutho wegazi ophezulu (ifomu kuphela ye-nephrogenic);
- ubukho beentlungu ezinzima kwindawo echaphazelekayo;
- ukuhlaziywa kwi-ureter, e-malorazvit.