Esinye sezifo ezidumileyo ezizimeleyo yi-myasthenia gravis. Esi sifo sichaphazela inkqubo ye-neuromuscular. Iimbangela ze-myasthenia gravis zingafani, kodwa iimpawu zesifo kwizinto ezininzi eziphilayo zifana. Esi sifo sidibene nokukhathala okwandayo kwimisipha yomzimba. I-Myasthenia gravis, bobabini nabasetyhini, kodwa njengokuba amava abonisa, isondo esifanelekileyo sesifo sifunde kakhulu.
Iimbangela ze-myasthenia gravis
Nangona ukuba isifundo sesi sifo siye saqhubeka iminyaka emininzi, ngokuqinisekileyo ukuba i-myasthenia gravis iqalile, iingcali azikwazi ukuthetha. Kucacile ukuba, ukufunyanwa kwezinto eziza kuzalwa kubandakanya indima ebalulekileyo ekuphuhlisweni kwesi sifo. Kungenxa yesi sizathu sokuba i-myasthenia gravis ingabonwa ngandlela-thile nakwiintsana. Nangona kunjalo, emva kweeveki ezimbalwa, kunye neentsuku, ukugula kwezingane kuyadlula.
Esinye isizathu esinokwenzeka se-myasthenia gravis sisifo se-thymus okanye thymus gland . Kule meko, ama-antibodies atholakala kwiiscuphe zelungu elonakalisa i-receptors ezempilo ezithatha inxaxheba kwiintambo ze-muscle fibers. Ezi zixhobo zokulwa ziza kwenziwa ngenxa yeziphazamiso ezenzeka kwiijethi zeeprotheni. Isizathu salo lonke le meko enganelisekiyo yenkqubo yomzimba.
Iimpawu ze-myasthenia gravis
Kukho iindlela ezintathu eziphambili ze-myasthenia gravis:
- jikelele;
- iliso;
- ibhola.
Bonke bangaba bantwaneni okanye bafumane kwaye baholele ekuphumuleni izihlunu ezibethekileyo. Oku kwenzeka kwiimeko ezininzi emva kokusebenza ngokomzimba.
Uphawu oluphambili lwe-myasthenia gravis limbono ombini. Ngokuhambelana nokubonakaliswa kwesi sifo, ukungabikho kokuzikhethela kweenkophe kungenziwa. Amehlo omguli aphelelwe ukhathala kunokoqobo, kwaye oku kuphawulwa ngokumalunga nemvelaphi yemithwalo eyaneleyo.
Kwiimeko ezininzi, kwindawo yokuqala, izihlunu zihlupheka, iimpembelelo ezondliwa ngokuthe ngqo kwiimbilini ze-cranial. Kwixesha elizayo, njengoko uphuhliso lwesifo luyakuchukumisa imisipha yentamo, izitho.
Ngokude i-myasthenia gravis ihlala ingakhange ingqalelo, iimpawu zesifo eso zivela. Uphawu oluqhelekileyo lwesi sifo lukwaphulwa kwesichazizwi. Izigulane ezininzi emva kokuzikhandla ngokwenyama zifumana ubunzima, zizama ukuzwakalisa amagama ambalwa kunye namazwi.
Ukongezelela, i-generalized, i-bulbar kunye ne-myasthenia gravis yamacandelo ingabonwa ngeempawu ezilandelayo:
- ukuphazamiseka komsebenzi wemoto kwimida ngokubanzi kunye neminwe ngokukodwa;
- ukuphulwa kwesigqi sokuphefumula;
- iingxaki ngokugwinya;
- kuncitshiswe ukusebenza kwenkqubo ye-musculoskelet;
- ukuhanjelwa rhoqo okanye ukuzithiba;
- ukuhlaselwa kwentliziyo esheshayo;
- Ukuphazamiseka emsebenzini wesimiso se-nervous system.
Kwi-bulbar ye-myasthenia, phakathi kwezinye izinto, kukho utshintsho kwintetho. Ilizwi lesigulane liba likhulu, liqhekeza, lidibanise kwaye lithe cwaka. Ifom epheleleyo jikelele yesifo
Kwizigaba zokuqala emva kokuphumla okufutshane, imeko yesigulane ibuyele ejwayelekile. Kodwa ekuhambeni kwexesha, iimpawu ze-myasthenia gravis ziya kuhlala nangemva kokuphumla ngokupheleleyo.
Ukujamelana nesi sifo kunokuba neziyobisi, ezibandakanya i-acetylcholine. Iindlela ezifanelekileyo ziyiProserin okanye i-Kalimin. Ukongezelela, i-corticosteroids kunye ne-cytostatics inokumiselwa. Ukuba kuyimfuneko, isigulane sisuswe i-thymus gland.