I-Myopathy - yintoni na?

I-Myopathy isifo apho ukuphela kwezibilini zesibindi kubangela ukuba imfucu ye-muscle ihlaziye, kwaye i-atrophy ye-muscle iyenzeka. Kuze kube kutshanje, kwakukholelwa ukuba isifo esinjalo, njengesifo sengqondo, sinomzuzwana kuphela. Nangona kunjalo, kuboniswa ukuba ukulimala kunye nokusuleleka, ukungabikho kwamavithamini, iinkqubo zokuvuvukala kungakhokelela nokuphuhliswa kwe-muscular dysstrophy.

Izibonakaliso zengqondo

Ukuphuhliswa kwesi sifo kuqale kwasebuncinaneni. Nangona kunjalo, ngezizathu ezingafaniyo zokuzalwa kwe-myopathy, uphuhliso lwayo lunokuthi lwenzeke kwiminyaka ekhulileyo.

Isigulane sinobuthakathaka kunye ne-atrophy ye-muscle kwindawo ethile. Ngokuxhomekeka kwimeko yesifo, ngokuyininzi izihlunu zebhande kunye neengxowa, kunye nezitho, zichaphazelekayo. Ukuphuhliswa kwe-atrophy kwenzeka ngokulinganayo. Ngokuchasene nale mvelaphi, amanye amaqela ezinamahlunu angakhutshwa ngokuxhomekeka ngenxa yeoli kunye nezicubu ezixhamlayo. Ezi zihlunu zandisiwe ziphezulu.

Ngoko, yintoni le myopathy, kwaye zeziphi izifo ezifunyenwe rhoqo, siya kuqonda ngakumbi.

Ngokuxhomekeke ekuguquleni kwemfuza yeembalo zeesifo ezithintekayo, kunye nobudala besigulane, i-myopathy ihlukaniswe ngeefom ezininzi.

Iintlobo ze-myopathy

Uhlobo lwe-Erb

Uhlobo lwe-Erb's myopathy luyabonakalisa lusondele ngakumbi kwishumi leminyaka yesibini kwaye luchaphazela izihlunu ze-pelvic, kwaye luya kwandisa ibhinqa. Ngokuqhelekileyo waphawula i-hyperlordosis - ukukhawulwa komlenze phambili ngenxa ye-atrophy yezihlunu zangasemva nesisu. Imisipha yomlenze yomlomo iyaphukileyo, imilomo igxothwe ngaphandle, isiguli asikwazi ukumomotheka. Iinguqulelo zitshintsho.

Myopathy yeBeker

I-mecopathy ye-Benecker ye-hypertrophic myopathy ichaphazela imisipha emilenze. Ukuqala kwesi sifo kuqhubeka ngokukhawuleza kunye nokwanda okubonakalayo kwimizimba ye-gastrocnemius kunye nokusabalala kwe-atrophy kwiqela le-muscle ye-hip.

Kwithuba elithile isigulane sinethuba lokunyakaza okuzimeleyo. Ngenxa yokwehla kwe-Becker, ukungaphumeleli kwentliziyo kuyimpawu .

Myopathy Landuzi-Dezherina

Ukubonakaliswa kwesi sifo kuqala ekufikeni kwentsha kwaye kubonakaliswe i-atrophy ye-facial muscle ebusweni. Kule meko, isigulane sineengxaki zomlomo, iibhokhwe aziwa, kwaye ubuso buso bunzima.

I-Atrophy isondela kwimisipha yamabhinqa ehlombe, kodwa amandla okusebenza agcinwa ixesha elide.

Myopathy kwiso

I-Myopathy kweso lihlehliswa ngokuthe gqolo ekuhambeni kwemehlo ezinobungozi obupheleleyo okanye obuncinane bombono, kwaye ngamanye amaxesha ukutshatyalaliswa kwe-pigmentation ye-retina kukhoyo. Iyiphi i-eye myopathy eyabonakaliyo ngokukhawuleza, ngokungahambiyo ikholelwa ukuba iimpawu ezinjalo zizibonakaliso zesilonda esisisiseko se-apula-oculomotor.

Kukho iintlobo ezimbini zokukhubazeka:

Kwimeko yesibini, izihlunu ze-pharynx zichaphazelekayo.

Myopathy

Xa ukusuleleka komzimba kunye neentlobo ezithile zeebhaktheriya kunye nokuvuvukala kwimizimba yamathambo, kukho imopathy, ebonakaliswa bubuthathaka emzimbeni, intlungu kwiimfucu, ukuvuvukala nokunyuka komsebenzi. Olu hlobo lwesifo lunokuphathwa nge-glucocorticosteids.

Kukho iintlobo ezahlukeneyo zokuzikhumbuza komzimba:

Unyango lwe-myopathy

Ngokuqhelekileyo, unyango luphawu, lujoliswe ku:

Faka isicelo se-physiotherapy, ukubhukuda kwe-gymnastics. Isiphumo esihle kukusetyenziswa kwezilwanyana ze-hormone ze-anabolic, i-ATP.

Zonke iinkqubo zenziwa ukunciphisa imeko yesigulane kunye nokunciphisa inkqubo yokuchithwa kwemisipha, kodwa ayifanelekanga kwaye ayichaphazeli inkqubo yesifo.