Unzima kakhulu ukuyiphatha izifo ezithintekayo ezinxulumene nokuguquka kwemfuyo. Ezi ntsholongwane ziquka i-cystic fibrosis, enokuxhaphaka ngokubanzi kunye nekhosi engapheliyo. Kukho iintlobo ezibalulekileyo zesi sifo, zihlelwe ngokuhambelana nommandla kunye nomlinganiselo wokutshatyalaliswa kwamalungu angaphakathi.
Yintoni i-cystic fibrosis okanye i-cystic fibrosis?
Isifo esichazwe ngumtshintsho wegciwane leCFTR elijongene nokuxutywa kwamanzi. Ngenxa yeenguqu zayo zentsholongwane, i-secretion ifihliwe, eyenziwa ngamaqela ahlukahlukeneyo emzimbeni. Ngenxa yokungena kwetyuwa ngokweqile kwiiseli, kunye nokuntuleka kwamanzi, ukugqithisa kwe-mucus kunzima kwaye kuhlala kwimizi, ukuvalela. Emva kwithuba elithile kwisayithi yezo "jams traffic".
Kukho iintlobo ezi-3 eziphambili ze-cystic fibrosis:
- bronchopulmonary;
- emathunjini;
- zixutywe.
Kukho ezinye iindawo ezichaphazela isifo, umzekelo, kukho i-cystic fibrosis ye-lacteal kunye ne-pancreas, i-sinanas paranasal. Akunakuthi zifumaneke, kodwa akukho nengozi ngaphantsi kweendlela ezilapha ngasentla zentsholongwane.
Iimpawu ze-cystic fibrosis
Iimpawu ze-cystic fibrosis zixhomekeke kwingingqi yesilonda kunye nesimo sesifo, kunye neqondo lokubandezeleka kwayo.
I-cystic fibrosis yemiphunga ibonakaliswe ngale ndlela:
- Ukuhlaselwa rhoqo kwesiqhwala esibuhlungu;
- ubunzima bokuhlula i-sputum;
- ukuphefumula okufutshane;
- i-bronchitis eqhubekayo;
- i-pneumonia ende;
- phuhliso lwe emphysema .
Ukubonakala kwamathumbu omzimba we-cystic fibrosis kuhambelana neempawu ezilandelayo:
- ukunyuka kwamanzi;
- izitulo eziqhelekileyo;
- ukucima ;
- ukubethelela intlungu ebuhlungu kummandla wamathumbu;
- phuhliso lweenkqubo zokulonda.
Ngokuqhelekileyo, ngale ndlela ye-cystic fibrosis, isibindi sichaphazelekayo. Oku kubangelwa ukuphulwa kwe-absorption kunye ne-excretion ye-bile emathunjini, ngenxa yesigxina sokuthi igxininisa kwiidonki,
Ifom ye-cystic fibrosis ixubile. Idibanisa iimpawu ze-bronchopulmonary kunye neentsholongwane zokugaya i-digestive pathology kanyekanye.
Unyango lwe-cystic fibrosis okanye i-cystic fibrosis
Akunakwenzeka ukukrazula ukugula okuchazwe ngonaphakade, nangona kunjalo, kunye neyeza elinokoqobo, uphawu lobomi bomntu one-cystic fibrosis luphuculwe kakhulu.
Ukongezelela kumayeza amiselwe ugqirha, isigulane kufanele senze kakuhle ukulungelelanisa ukutya okunomsoco, rhoqo ukwenza umzimba okhethekileyo, umzimba wokuphefumula.