I-Reye's syndrome

Isifo sikaRay (okanye iReye) asizange sibe sisifo esifanayo. Le ngxaki ayifumaneki, kodwa ibangela ingozi enkulu emzimbeni. Kukholelwa ukuba oku kugugu kwabantwana. Kuxilongwa ngokugqithiseleyo kwiminyaka eyi-15. Kodwa amatyala amaninzi, xa i-syndrome ibetha kunye nabantu abadala, amayeza ayaziwa. Ngoko, esi sifo "asiyikunyelisa" nabani na.

Izizathu zeReye's Syndrome

Ngesihlandlo sokuqala isifo safunyanwa ngo-1963. Ukususela ngoko, kuye kwafunyaniswa kwizingane eziliqela eziliqela ngonyaka. Kodwa ngoku akukho mntu uye wakwazi ukubona izizathu zesifo.

Kukho ukuphakama okuphezulu ukuba i-Acetylsalicylic Acid ithintela uphuhliso lwe-Ray's syndrome. Okanye, ngokuchanekileyo, ukwanda komzimba kule nkunkuma. Iingcali zafika kwesi sigqibo, ngenxa yokuba isininzi sisifo sifumaneka kwizigulane ezineenkukhu, imasel, umkhuhlane, izifo zokuphefumula kunye nezinye izifo ezihambisana nomkhuhlane, umkhuhlane, umkhuhlane. Bonke bathatha i-Aspirin ngamanqanaba amatshitshisilo ukuze baququzelele impilo yabo.

I-Acetylsalicylic acid emva kokungena emzimbeni ngokukhawuleza kuthintela izakhiwo zamaselula. Kwaye, oku, kukhokelela ekuphazameni kwi-metabolism ye-acid acids. Ngenxa yoko, ukungena kwe-fatty of liver kukhula, kwaye izicubu zelungu ziqala ukuhlakala. Yingakho iingcali zibiza lo bhubhane lwe-syndrome hepatic encephalopathy.

Ichaphazela i-Reye's syndrome kunye nomsebenzi wengqondo. Ukuvuvukala kwakhe kuqala. Ngokufanayo, inkqubo ye-nervous central iphendula kwisifo. Kwaye isifo sifana nazo zonke iinkqubo ezihamba ngokukhawuleza.

Iingcali zikholelwa ukuba i-Ray's syndrome inokufumana ilifa. Okokuthi, ukuba umntu ovela kwisihlobo segazi uye wafumanisa ukuba unesifo, izifo ezithile ze-metabolic zingasungulwa emzimbeni ngexesha lokuzalwa. Ngenxa yezi ngxaki emzimbeni, ezinye i-enzyme zilahlekile okanye azisebenzi kakuhle, kwaye ngenxa yoko, i-fatty acids ayidilizi.

Iimpawu zeRay's Syndrome

Intsimbi yokuqala yokuxhalaba kufuneka ibe kukuhlaselwa isicupucu esinokuhlanza kakhulu. Nge-encephalopathy ye-hepatic, inani le-glucose egazini lehla ngokukhawuleza. Ngako oko, isigulane sixhatshazwa bubuthathaka, ukugungqeleka okukhulu, ukunyaniseka, ngezinye izihlandlo - ukulahleka kwengqondo kunye neenkampu. Ukongeza, kunye ne-Ray's syndrome kubantu abadala, kunokuthi kubekho:

Ukuxilongwa, unyango kunye nokukhusela i-Ray's syndrome

Olunye uhlalutyo olunjalo, oluya kubonisa ubukho be-Ray's syndrome, cha. Ukuze wenze ukuxilongwa, kufuneka unikeze i-lumbar puncture, i-biopsy yolusu kunye nesibindi, ukuhamba ngekhompyutheni kunye nokucatshulwa kwemifanekiso emagnini, uthathe iimvavanyo zegazi.

Injongo ephambili yonyango kukuthintela ukutshabalaliswa kwesibindi kunye nokuphulwa kwemisebenzi yayo. Ngenxa yoko, izigulane zijojowe nge-glucose. Ukongeza kwezi zinto, unyango luquka ukulawulwa kwe-mannitol, i-corticosteroids kunye ne-glycerin. Ezi zinto zinceda ukususa i-edema ye-cerebral. Kwaye ukuba unyango luphumelele, kubaluleke kakhulu kwi-syndrome kaRay ukuyeka ngokupheleleyo ukuthatha i-Aspirin nazo zonke iziyobisi ezine-acetylsalicylic acid.

Iziganeko ze-encephalopathy ye-hepatic ayikho eyona nto ifanelekileyo. Ngesiqingatha seemeko, eso sifo sikhokelela ekufeni. Kodwa ukuba unyango luqaliswa ngexesha, isibindi kunye nemisebenzi yengqondo zibuyiselwa ngokukhawuleza.