Isifo esisisifo seentsana ezisanda kuzalwa

Abanye abantwana phakathi kweeyure ezingama-24 neye-72 babonisa imeko yokugula - ukwanda kwamanzi ukusuka kwilonda elibi, isisu, isisu. Iqela leemeko ezifanayo zivela kwi-0.2-0.5% yeentsana zibizwa ngokuba zizifo ezibangelwa i-neonatal disease. Ngokuqhelekileyo, esi sifo sisiphumo sokungabikho kwe-vitamin K emzimbeni. Kwiintsana ezizalwayo, isifo singabonakala kwiveki yesithathu yobomi. Oku kubangelwa kubukho ebusweni lwe-thromboplastin-into yokucima igazi. Isifo esinyamekayo sentsana esabonakala kulo mhla sithathwa njengexesha elide.

Kukho iintlobo ezimbini zezi zifo: ukuhlaziywa okuphambili kwiintsana ezisanda kuzalwa, ukuphuhliswa kobunqongophala be-vitamin K, kunye nokusekondari, apho i-preterm kunye nabantwana ababuthathaka abanezinto ezinobuthakathaka obunobungozi obusebenzayo. Phantse ama-5% ezintsana zifumana ubunzima obuncitshisiweyo be-K-vitamin-dependant factors, uma umama ngexesha lokukhulelwa wathabatha i-antibiotics, aspirin, i-phenobarbital okanye i-anticonbulsant drugs ezichaphazela umsebenzi we-hepatic. Kwinqanaba elijongene nobungozi banabantwana abanoomama abanesifo se-toxicosis, i-enterocolitis kunye ne-dysbacteriosis ngasekupheleni kwexesha.

Umfanekiso wekliniki kunye nokuxilongwa

Eyona nto iphezulu ye-diathesis, abantwana banamava, isisu sisisu, ukutyumla kwesikhumba, kunye nokutyumla. Ukubonakalisa okunjalo kwesikhumba kuthiwa yi-purpurea kumayeza. Ukuxilongwa kwegazi lomzimba kuqhutyelwa kwisihlalo - isitulo kwi-diaper ibumnyama kunye nomtya wegazi. Ngokuqhelekileyo oku kuhamba kunye nokuhlanza igazi. Ngokuqhelekileyo, ukuphuma kwamathumbu emathunjini angatshatanga. Ifom ehamba phambili ihamba kunye nokuphuma kwegazi kwi-anus, ukuhlanza okuqhubekayo kwegazi. Ngamanye amaxesha ugalelo lwegazi luya kwenzeka. Ngelishwa, imiphumo yesifo esiyingozi seentsana ezisandul 'ukuzalwa ngokungabikho kokunyamekela ngonyango ngexesha elifanelekileyo liyabulala - umntwana uswelekile. Ifom yesibili yesifo ibonakaliswe ngobungqina besifo kunye ne- hypoxia . Ukongezelela, i-cerebral hemorrhage, imiphunga, kunye neengxenyana zengqondo ziyafumaneka.

Ukuxilongwa kwezifo ezithintekayo kwiintsholongwane kusekelwe kwidatha yeklinikhi kunye neziphumo zezifundo ezilandelayo (igazi le-smear, i-thrombotest, isibalo seplatelet, umsebenzi wezinto zokuqhawula kunye ne-hemoglobin). Ngexesha elifanayo, usana olutsha luvavanyelwa ezinye i-diathesis enobunzima: i-hemophilia, isifo se-Willebrand, i-thrombastenia.

Unyango kunye nokuthintela

Ukuba inkambo yesi sifo ayinakunzima, ngoko-ke ukugqithisa kubonakala kulungile. Kwixesha elizayo, ukuguqulwa kwezinye iintlobo zezifo eziqhekezayo azikho.

Ukunyangwa kwanoma yikuphi ukuphuma kwamanzi kubomi bokuqala bokuqala ubomi buqala ngejoyi ye-intramuscular ye-vitamin K, apho umzimba unako. Kubalulekile ukujonga i-thrombotest ukujonga ukulungelelaniswa kwezinto ezixhomekeke kwi-vitamin-dependent factors. Kwiintsuku ezintathu ukuya kwezine, umntwana ulawulwa yi-vikasol, kwaye kwiimeko ezinzima, ukunyuka kwamanzi kwiplasma (esandulisiwe) kunye nokulawulwa ngokufanayo kwe-vitamin K kulawulwa. I-plasma ilawulwa ngesilinganiso sama-milliliters ayi-10 kilogram yesisindo somzimba. Ulwaphulo lwempawu lwenziwa kuphela kumaSebe akhethekileyo.

Ukuthintela kwesi sifo kuqulethwe enye i-Vikasol kwiintsana, ezazalwa ngokukhulelwa kunye ne- toxicosis . Kwiprophylaxis efanayo, iintsana nazo ziyafuneka kwiimeko ze-asphyxia ngenxa yexinzelelo oluthathaka okanye ukusuleleka kwe-intrauterine.

Abasetyhini abanezifo ezahlukileyo kwixesha elidlulileyo ezidibeneyo nokunyuka kwegazi kufuneka zihlolwe xa zikhulelwe.