I-neuroblastoma ye-retroperitoneal space

I-neuroblastoma isifo esibi esichaphazela isistim se-nervous sympathetic system. Ngokuqhelekileyo, i-tumor ivela kubantwana ukuya kwiminyaka emibini kwi-retroperitoneal space. Kule meko, ukuphuhliswa kwesi sifo kuqala ngeengqungquthela ze-adrenal. Kwakhona, i-tumor yokuqala ingathintela izicubu kunye nomlenze womntwana - kwindawo yesifo se-thoracic kunye nentloko yomlomo.

Izizathu zokubonakala kwe-neuroblastoma

Kuze kube ngoku, izazinzulu azikwazi ukuchaza ngokucacileyo isizathu sokuba esi sifo esiyingozi sibonakale. Kuyaziwa ukuba i-neuroblastoma ivela kwiiseli zamama-embryonic, i-neuroblast. Iingcambu zesifo zilele kwi-heredity kunye nokuguqulwa kweeseli. Kwezinye iimeko, ukuvuvukala kumntwana kungabonwa ngexesha lokuhamba kwe-ultrasound.

Ziziphi iimpawu ze-neuroblastoma ye-retroperitoneal?

Isisu esibi kakhulu sinokugquba kwaye singakhula ngokukhawuleza, okukhokelela ekubunjweni kwamathambo. Nangona kukho iimeko xa ukunyanga ngokukhawuleza kwaqala ngaphandle kokungenelela kwezokwelapha. Kwakhona, kwezinye izigulane, iiseli ezibi zaguqulwa zibe ngamaseli angenayo.

I-neuroblastoma ye-retroperitoneal space isikhombisa ukwanda kwisisu somntwana, ngokuqhelekileyo kubangele intlungu kwisisu esiswini.

Ngokuqhelekileyo, i-tumor ibangela ukukhukhumeza, ukusebenza kakuhle kwe-intestine kunye nesisu. Ubushushu bomzimba kunye noxinzelelo lwegazi lunokwanda. Ukongezelela, umntwana usenokuphelelwa ngumdla, ulahlekelwe isantya ngokukhawuleza.

I-Neuroblastoma

Ukuze ubeke i-diagnostic eyiyo nge-neuroblastoma kwaye uqale unyango oluchanekileyo, kuyimfuneko ukuqhuba ukuxilongwa ngokupheleleyo. Nge-neuroblastoma, uvavanyo lwakhe lwe-hertological usetyenziswa ngokubanzi, zombini i-tumor ngokwayo kunye ne-metastases.

Kubalulekile ukuqonda isigaba sesi sifo si-ultrasound kunye ne-tomography.

Izigaba ezine ze-neuroblastoma ye-retroperitoneal

Inkqubo eqhubekayo yokonyango kunye nesiphumo sayo ngokuthe ngqo kuxhomekeke kwisigaba sesifo. Kuyavunyelwa ukuhlukanisa izigaba ezine zekhosi yesi sifo. Kodwa ufanele ukwazi ukuba ukuba isifo siyaphathwa kakuhle kwisigaba sokuqala okanye sesibini, amathuba ancitshiswa kakhulu kwisigaba sesithathu nesine. Makhe siqwalasele ngokubanzi.

  1. ² isigaba. Ukususwa kokukhwabanisa kwendlela yokwenza kakubi.
  2. ІІA isigaba. Mhlawumbi ukususwa ngokukhawuleza kweninzi ye-neuroblastoma.
  3. IIB. I-neuroblastoma ingaba yodwa. Kukho ithuba lokususa ngokupheleleyo, okanye ubuninzi balo.
  4. UMSEBENZI isigaba. Kule nqanaba, i-tumor ingaba linye, linye, okanye libethe icala. Kwakhona kubonakaliswe izidumbu kwi-lymph nodes. Ayikwazi ukugcina ngaphezulu kwama-55-60% wabantwana.
  5. IV. Ukutshatyalaliswa kweentlobo ze-metastase kwii-lymph nodes, izicubu zethambo nezinye izitho. Ingasinda ngaphezu kwekota yesigulo sabantwana abagulayo.
  6. IVS. Ubonakaliswe ngamathambo kwisigaba sokuqala nesibini, kwaye sichaphazela isibindi, isikhumba kunye namathambo esifuba.

I-neuroblastoma isifo esiyingozi kakhulu. Iindlela eziphambili zonyango - ukususwa ngokukhawuleza kwemfundo enobungozi, i- chemotherapy kunye neyeza zonyango.

Kuxhomekeke kwisigaba sesifo, unyango oluthile lusetyenziswa. Ukuba eso sifo sisesigaba sokuqala okanye sesibini, njengomthetho, ukungenelela kokuphaphaza kunye ne-chemotherapy yangaphambilini imiselwe. Isigaba sesithathu sokuphuhlisa i-tumor ayinakusebenza, ngoko umntwana unikwe i-chemotherapy. Kwinqanaba lesine, inkqubo yokuhlinzwa yenziwa ngokulandelwa ngethambo lomtshini wokutsalwa. Kubalulekile ukuchonga isifo ngexesha. Ekuqaleni amanyathelo athatyathwa, aphezulu amathuba okubuyiswa.