I-muscular dystrophy

I-muscular dysstrophy yiqela leempilweni ezingenasiphelo ezichaphazelekayo ezichaphazela izihlunu zomntu. Ezi zifo zibonakaliswe ngokunyusa ubuthathaka obunamahlunu, kunye nokuguqulwa kwezihlunu. Balahlekelwa yikhontrakthi, bathathe indawo kunye nezicubu ezinamafutha kunye nezidumbu kwaye zidibanise.

Iimpawu ze-muscular dystrophy

Kwizigaba zokuqala, i-muscular dysstrophy ibonakala ngokuncipha kwetoni ye-muscle. Ngenxa yoko, inzuzo ingaphulwa, kunye nexesha, ezinye izakhono zomzimba ziyalahleka. Ngokukhawuleza esi sifo siyaqhubeka kubantwana. Ngeenyanga nje ezimbalwa banokuyeka ukuhamba, behleli okanye baphethe intloko.

Kwakhona iimpawu ze-dysstrophy ye-muscular zi:

Iifomu ze-muscular dystrophy

Zininzi iintlobo zesifo esi saziwa namhlanje. Makhe siwaqwalasele ngokubanzi.

Duchenne muscular dystrophy

Le fom ibizwa nangokuthi i-pseudohypertrophic muscular dystrophy, kwaye idla ngokubonakalayo ebuntwaneni. Imiqondiso yokuqala yokugula ibonakala kwiminyaka engama-2-5. Ngokuqhelekileyo, izigulane zivakalela ubuthathaka kumaqela emisipha yombhobho we-pelvic kunye neenyawo ezingaphantsi. Emva koko bachatshazelwa yimisipha yesigxina esiphezulu somzimba, kwaye kuphela ke onke amaqela emisipha.

I-muscular dysstrophy yale fomu ingakhokelela ekubeni ineminyaka eyi-12 umntwana uya kulahlekelwa ngokupheleleyo. Uneminyaka engama-20, ezininzi izigulane azihlali.

I-dystrophic ye-muscular dystrophy ye-Erba-Rota

Olunye uhlobo lwesifo. Iimpawu zokuqala zesifo zibonakala ngokubonakalayo kwiminyaka eyi-14-16, kwiimeko ezinqabileyo-kwi-5-10 ubudala. Iimpawu zokuqala ezibonakalayo ziyinkxalabo yesifo sengqondo kunye nokutshintsha okubukhali kwi-"dada".

I-muscular dystrophy ye-Erba-Rota

Esi sifo sitholakala kuqala kwiimigca yama-muscle yeziphelo ezingezantsi, kodwa ngamanye amaxesha zichaphazela zombini iigxala kunye nezihlunu ze-pelvic kanyekanye. Isifo siyaqhubeka ngokukhawuleza kwaye sibangela ukukhubazeka.

Becker dystrophy muscular

Kuyafana nempawu ngefomu yangaphambili yesifo, kodwa le fomu iqhubela phambili. Isigulane sinokuhlala sisasebenza iminyaka emininzi.

I-Emery-Dreyfus muscular dystrophy

Olunye uhlobo lwesifo esicatshungulwayo. Le fomu ibonakala phakathi kweminyaka emi-5 no-15 yobomi. Iimpawu zokuqala zesifo se-muscular dystrophy zi:

Izigulana nazo zinokuba nokuziphatha komzimba kunye nokunyamekela umzimba .

Unyango lwe-muscular dystrophy

Ukuxilonga i-muscular dystrophy, uviwo kunye ne-orthopedist lwenziwa, kwaye i-electromyography yenziwe. Unokuqhuba isifundo se-biological molecules esiza kunceda ukucacisa ukuba kungenzeka ukuba isifo kubantwana.

Ukunyangwa kwe-muscular dystrophy yinto eyenzelwe ukunciphisa nokuyeka inkqubo ye-pathological, kuba akunakwenzeka ukuphilisa ngokupheleleyo le ngxaki. Ukuthintela ukuphuhliswa kweenkqubo ze-dysstrophic in the muscles, isigulane sinikezwa iinjenges:

Isigulane kufuneka senze rhoqo ukuhlalisa umzimba.

Kwakhona, wonk 'ubani ojongene ne-muscular dysstrophy, kufuneka wenze ukuphefumula okuvuthayo. Ngaphandle kwayo, izigulane ziza kuhlakulela izifo ezinjalo zokuphefumula njenge-pneumonia kunye nokungaphumeleli kokuphefumula, kwaye kubekho nezinye iingxaki: