Impilo enempilo ikhuselwe ngamajoni omzimba omzimba ukusuka ekuhlaselweni kwintsholongwane, i-fungal kunye ne-bacterial, i-allergen nezinye izinto ezingathandekiyo. I-immunodeficiency yeprayimari yamandulo iyanqanda umntu wale mngcawu ukusuka kwiminyaka yokuqala yobomi, kodwa unokuzibonakalisa ebuntwini. Esi sifo sidinga ukubeka esweni rhoqo ngugqirha kunye nonyango olude kakhulu.
Ulwahlulo lwezonyango zokuqala ezingabantwana bokuzalwa
Ubuthakathaka obuphantsi kokucatshungulwa luhlobo lwe-5 iintlobo, ezibangelwa ukungapheli:
1. Ukungakwazi ukukhubazeka kwamaselula:
- oroticide;
- isifo seDi Georgi;
- fermentopathy exhomekeke kwi-biotin;
- ukungakwazi ukusebenza kwe-purinucleoside phosphorylase.
2. I-Phagocytic primary immunodeficiency:
- isifo esingapheliyo;
- i-cyclic ne-chronic acyclic neutropenia;
- I-Miller's syndrome ("i-leukocytes enobuqili".
3. Ukungapheli kwamaseli e-humoral:
- ukuqala komzimba wokuqala;
- Isifo sikaBruton;
- ukunyuka kokukhetha kwama-immunoglobulins.
4. Ukusilela kokuhlanganiswa kwamagciwane omzimba kunye nokuziphatha komzimba:
- Isifo seWiskott-Aldrich;
- i-hypocalcemia ;
- dysgenesis
- I-Glanzmann-Riniker syndrome.
5. Ukungaphumeleli okuhambelanayo:
- Edema ka-Quincke-Osler;
- lupus erythematosus;
- i-rheumatoid arthritis.
Iimpawu ze-immunodeficiency
Akukho zibonakaliso ezibonakalisa ukuvumela ukuchaneka ngokuchanekileyo ukuchazwa kwemfuyo yezofuzo. Ukubonakaliswa kwezonyango kuyahluke kakhulu kuxhomekeke kumhlobo, ukuma kunye nokuqina kwesi sifo.
Ukukrokraza i-immunodeficiency eyinqanaba eliphambili kunokwenzeka kwiimpawu ezinjalo:
- ukukhutshwa kwezifo ezithathelwanayo kunye nezifo zentsholongwane;
- umphumo omncinci wokuthatha i-antibiotics;
- candidiasis yesikhumba kunye nokubuya kwakhona;
- ukugqithisa;
- i-pneumonia 2 kunye namaxesha angaphezulu ngonyaka;
- u-otitis osisigxina, i-sinusitis, i-bronchitis.
Unyango lwe-immunodeficiency
Unyango luyinkimbinkimbi, kuba awukwazi ukuphilisa i-pathology. Ukuphucula umgangatho wobomi bezigulane, unyango oluqhubekayo lwe-immunosubstitutional ne-immunoglobulins luyimfuneko, kunye nokukhethwa ngokuchanekileyo kwe-antibacterial, anti-antial and antitimycotic agents.
Ulwaphulo olunzulu lwezifo ezichazweyo luquka ukutsalwa kwethambo lomnkantso, okwenza ngcono xa usencinane. Kodwa kubalulekile ukuba uqaphele ukuba lo msebenzi ubiza kakhulu, kwaye ngamanye amaxesha kunzima ukufumana umniki-mali ngokuhambelana okwaneleyo.